DIAGNOSIS BANDING TUMOR JARINGAN LUNAK Pembimbing: dr. Ooki Nico Junior S! B"K#Onk Ke!$ni%er$$n Bed$& RSUD 'i$(i
KLASI)IKASI TUMOR JARINGAN KLASI)IKASI LUNAK * Adi!oc+c Adi!oc+c%ic %ic Tumor Tumor Benign
Lipoma Lipomatosis Lipomatosis of nerve Lipoblastoma / lipoblastomatosis Angiolipoma Myolipoma of soft tissue Chondroid lipoma Extra-renal angiomy angiomyolipoma olipoma Extra-adrenal myelolipom myelolipomaa Spindle cell / pleomorphic lipoma Hibernoma
Intermediate (localy aggressive)
Atypical lipomatous tumour / ell differentia differentiated ted liposarcoma Malignant
!edifferentiated liposarcoma !edifferentiated Myxoid liposarcoma "leomorphic liposarcoma
KLASI)IKASI TUMOR JARINGAN KLASI)IKASI LUNAK * )ibrob,$-%i )ibrob,$-%ic c m+o/ibrob,$m+o/ibrob,$-%ic %ic %umour-
KLASI)IKASI TUMOR JARINGAN LUNAK * )ibrob,$-%ic m+o/ibrob,$-%ic %umour-
KLASI)IKASI TUMOR JARINGAN LUNAK * So0c$,,ed /ibro&i-%ioc+%ic %umour-
* Smoo%&0mu-c,e %umour-
KLASI)IKASI TUMOR JARINGAN LUNAK * Peric+%ic "!eri1$-cu,$r# %umour-
* Ske,e%$,0mu-c,e %umour-
KLASI)IKASI TUMOR JARINGAN LUNAK * 2$-cu,$r %umour-
KLASI)IKASI TUMOR JARINGAN LUNAK * G$-%roin%e-%in$, -%rom$, %umour-
* Ner1e -&e$%& %umour-
KLASI)IKASI TUMOR JARINGAN LUNAK * Tumour- o/ uncer%$in di//eren%i$%ion
KLASI)IKASI TUMOR JARINGAN LUNAK * Tumour- o/ uncer%$in di//eren%i$%ion
Adi!oc+%ic Tumour* Ke,om!ok %erbe-$r d$ri %umor me-enc&+m$, k$ren$
%inggin+$ !re1$,en-i ,i!om$ d$n $ngio,i!om$. * Li!o-$rcom$ meru!$k$n -$rcom$ 3$ring$n ,un$k +$ng
!$,ing umum. * Sec$r$ -ub%+!e 4i-%o,ogi- u%$m$n+$ beru!$ (e,,
di//eren%i$%ed m+5oid d$n !,eomor/ik -e!enu&n+$ memi-$&k$n !en+$ki% ini -ec$r$ mor/o,ogi +$ng berbed$
Li!om$ De/ini-i *%umor 3in$k +$ng %erdiri d$ri (&%e $di!oc+%e- m$%ur d$n
meru!$k$n %umor 3$ring$n ,un$k +$ng !$,ing -ering !$d$ or$ng de($-$. 6!idemio,ogi *-ering !$d$ u-i$ 78 0 98 %$&un J$r$ng !$d$ $n$k0$n$k *Obe-i%$-
Li!om$ Si%e o/ in1o,1emen% * 3$ring$n -ubku%$n ",i!om$ -u!er/i-i$,# * 3$ring$n ,un$k d$,$m "dee! -e$%ed ,i!om$# Li!om$
in%r$mu-ku,$ri- "b$%$ng %ubu& ke!$,$ d$n ,e&er b$gi$n $%$- d$n ek-%remi%$- b$($
Li!om$
in%ermu-ku,$ri- "dinding $bdomen#
*!ermuk$$n %u,$ng "P$ro-%e$, ,i!om$# *Li!om$ $rbore-cen-. "S+no1i$, ,i!om$#
Li!om$
Li!om$ M$ni-/e-%$-i K,ini*M$--$ 3$ring$n ,un$k %$n!$ di-er%$i n+eri "kec ,i!om$
ukur$n be-$r +$ng mengen$i -$r$/ !eri/er# *Pembengk$k$n -endi " Li!om$ $rbore-cen-#
M$kro-ko!i *berb$%$- %eg$- *Ukur$n ; cm ",i!om$ -u!er/i-i$,# <;cm "dee! -e$%ed
,i!om$# *ber($rn$ kuning *Po%ong$n !ermuk$$n +$ng bermin+$k.
Li!om$
Li!om$%o-iPer%umbu&$n ber,ebi& di/u- 3$ring$n $di!o-$ m$%ur 6!idemio,ogi *bi$-$n+$ %imbu, !$d$ umur dib$($& = %$&un "Li!om$%o-i- di/u-# *,$ki0,$ki berku,i% &i%$m di ki-$r$n umur >0?8 %$&un."Li!om$%o-i!e,1ik# *!er%eng$&$n umur !$d$ ,$ki0,$ki medi%er$ni$n deng$n ri($+$% !en+$ki% &$%i $kib$% kon-um-i $,ko&o, ber,ebi&$n."Li!om$%o-i-ime%rik# *%er$!i &ormon$, $%$u !eningk$%$n !roduk-i $drenokor%ik$, -%eroid "Li!om$%o-i- -%eroid# *Ter$!i !ro%e$-e in&ibi%or !$d$ or$ng AIDS d$n %er$!i $n%ire%ro1ir$, "4I20,i!odi-%ro/i#
Li!om$%o-iSi%e- o/ In1o,1emen% *Li!om$%o-i- di/u- "ke%erk$i%$n deng$n m$crod$c%+,+
gig$n%i-me# : b$%$ng %ubu& -eb$gi$n gig$n%i-me# -eb$gi$n be-$r ek-%remi%$- ke!$,$ d$n ,e&er !eru% !$nggu, $%$u 3$,ur in%e-%in$, *Li!om$%o-i- -ime%rik : de!o-i-i -ime%ri- ,em$k di $%$-
b$gi$n %ubu& %eru%$m$ ,e&er. *,i!om$%o-i- !$nggu,: d$er$& !eri1e-ic$, !eri1e-ic$, d$n d$n !erirec%$ !erirec%$,. ,. *Li!om$%o-i- -%eroid -%eroid : ($3$& d$er$& -%ernum $%$u
!unggung "Bu//$,o "Bu//$,o &um!#. &um!#. *4I20,i!odi-%ro/i : $kumu,$-i d$ri ,em$k 1i-cer$, $di!o-i%
!$+ud$r$ -er1ik- ($3$& d$n $nggo%$ b$d$n.
Li!om$%o-i-
Li!om$%o-iM$ni/e-%$-i k,ini*Neuro!$%i *Ob-%ruk-i ,$ring *Kom!re-i d$ri 1en$ c$1$ *Menge,u& -$$% berkemi& *N+eri !$d$ !erineum *Sembe,i% *N+eri !$d$ $bdomen d$n !unggung *Ob-%ruk-i u-u*4idrone/ro-i-
Li!om$%o-iM$kro-ko!i *Le-i b$%$- kur$ng %eg$- deng$n $greg$% ,em$k ber($rn$
kuning ,embu% +$ng iden%ik deng$n !en$m!i,$n norm$, ,em$k. *S$%u0-$%un+$ !erbed$$n $d$,$& ,ok$-i ke%er,ib$%$n d$n
di-%ribu-i ,em$k.
A%+!ic$, %umor ,i!om$%ou- "ALT# (e,,di//eren%i$%ed "@D# Li!o-$rkom$ De/ini-i *neo!,$-m$ me-enc&+m$, g$n$- +$ng %erdiri -eb$gi$n $%$u -e!enu&n+$ !ro,i/er$-i $di!oc+%ic m$%ur +$ng menun3ukk$n 1$ri$-i -igni/ik$n d$,$m ukur$n -e, d$n -e%id$kn+$ $k%i!ik nuk,e$r /oc$, di kedu$ $di!o-i% d$n -%rom$ -e,. 6!idemio,ogi *7807; d$ri -emu$ ,i!o-$rkom$ *!erb$nding$n !ri$ d$n !erem!u$n -$m$ *%er3$di !$d$ !$ru& b$+$ de($-$ !unc$kn+$ dek$de ke 9 *L$ngk$ !$d$ $n$k0$n$k
A%+!ic$, %umor ,i!om$%ou- "ALT# (e,,di//eren%i$%ed "@D# Li!o-$rkom$ Si%e o/ in1o,1emen% *-ering %er3$di !$d$ 3$ring$n ,un$k d$,$m $nggo%$ b$d$n
%eru%$m$ !$&$ diiku%i o,e& re%ro!eri%oneum d$er$& !$r$%e-%iku,$r d$n medi$-%inum *D$!$% %imbu, did$er$& -ubku%$n *S$ng$% 3$r$ng !$d$ ku,i%
M$ni/e-%$-i k,ini*m$--$ +$ng membe-$r %$n!$ r$-$ -$ki% +$ng !er,$&$n0
,$&$n bi-$ menc$!$i ukur$n +$ng -$ng$% be-$r $-im!%om$%ik. "!$d$ re%ro!eri%oneum d$!$% menc$!$i di$me%er =8cm#
A%+!ic$, %umor ,i!om$%ou- "ALT# (e,,di//eren%i$%ed "@D# Li!o-$rkom$ M$kro-ko!i *m$--$ be-$r ber,obu- d$n berb$%$- %eg$- *m$--$ mu,%i!,e +$ng -$,ing %id$k ber&ubung$n. "bi$-$n+$
!$d$ re%ro!eri%oneum# . *@$rn$ ber1$ri$-i d$ri ($rn$ kuning -$m!$i !u%i& * Are$ nekro-i- ,em$k -ering di%emuk$n !$d$ ,e-i +$ng ,ebi&
be-$r.
Nodu,$r )$cii%iDe/ini-i *m$--$ +$ng %erben%uk d$ri !ro,i/er$-i /ibro-$ +$ng bi$-$n+$ %er3$di !$d$ 3$ring$n -ubku%$n. 6!idemio,ogi *-emu$ ke,om!ok umur %$!i ,ebi& b$n+$k -ering !$d$ or$ng de($-$ mud$. *in%r$1$-ku,$r /$-cii%i- d$n /$-cii%i- kr$ni$, 3$r$ng %er3$di. *In%r$1$-ku,$r /$-cii%i- di%emuk$n keb$n+$k$n !$d$ or$ng di b$($& 8 %$&un *)$-cii%i- kr$ni$, berkemb$ng %eru%$m$ !$d$ b$+i di b$($& u-i$ = %$&un d$n ,ebi& -ering !$d$ $n$k ,$ki0,$ki
Nodu,$r )$cii%iSi%e o/ In1o,1emen% *Subku%$n me-ki!un %erk$d$ng in%r$mu-ku,$r. *,ok$-i !$d$ ku,i% -$ng$% 3$r$ng. *Sering !$d$ ek-%remi%$- $%$- b$%$ng %ubu&ke!$,$ d$n
,e&er *in%r$1$-ku,$r /$-cii%i- 3ug$ -ubku%$n. %er3$di !$d$
!embu,u& d$r$& keci, &ingg$ -ed$ng *Kr$ni$, /$-cii%i- bi$-$n+$ me,ib$%k$n b$gi$n ,u$r d$ri
%engkor$k d$n 3$ring$n ,un$k +$ng berdek$%$n d$ri ku,i% ke!$,$ d$n d$!$% men3$,$r ke b$($& me,$,ui ,$!i-$n b$gi$n d$,$m ke meningen-.
Nodu,$r )$cii%i-
M+o-i%i- o--i/ic$n- d$n /ibroo--eou!-eudo%umour o/ digi%M+o-i%i- o--i/ic$n- "MO# d$n !-eudo%umor /ibroo--eoudigi% ")P# %er,ok$,i-ir -e,/ ,imi%ing ,e-i re!$r$%i/ +$ng %erdiri d$ri re$k-i &i!er-e,u,er 3$ring$n /ibro-$ d$n %u,$ng. 6!idemio,ogi *u-i$ +$ng ,u$- mu,$i d$ri b$+i -$m!$i $k&ir de($-$ "C7 0>; %$&un# *de($-$ mud$ "u-i$ r$%$0r$%$ = %$&un# * 3$r$ng %er3$di !$d$ b$+i $%$u or$ng %u$ *Pri$ ,ebi& b$n+$k d$ri!$d$ !erem!u$n ": =# *!erem!u$n ,ebi& b$n+$k %er,ib$% di )P. *P$-ien deng$n MO bi$-$n+$ $k%i/ -ec$r$ /i-ik.
M+o-i%i- o--i/ic$n- d$n /ibroo--eou!-eudo%umour o/ digi%Si%e o/ In1o,1emen% *MO berkemb$ng di ,ok$-i +$ng !$,ing ren%$n %er&$d$!
%r$um$ -e!er%i -iku !$&$ !$n%$% d$n b$&u. *)P bi$-$n+$ mem!eng$ru&i 3$ring$n -ubku%$n !rok-im$,
!&$,$n5 3$ri %$ng$n d$n 3$r$ng di 3$ri03$ri k$ki. M$ni/e-%$-i k,ini*Bengk$k d$n N+eri "C0= minggu# *=09 minggu n+eri meng&i,$ng
M+o-i%i- o--i/ic$n- d$n /ibroo--eou!-eudo%umour o/ digi%M$kro-ko!i *m$--$ o1$, ber($rn$
cok,$% deng$n !u-$% berki,$u ,embu% d$n deng$n !inggir$n $bu0 $bu0!u%i& ber!$-ir *ker$*Le-i berukur$n =0C= cm
"keb$n+$k$n -eki%$r ; cm#.
M+o-i%i- o--i/ic$n- d$n /ibroo--eou!-eudo%umour o/ digi%-
M+5o/ibro-$rcom$ %erdiri -!ek%rum d$ri ,e-i /ibrob,$-%ik g$n$- deng$n 1$ri$be, -%rom$ m+5oid !,eomor/i-me d$n deng$n !o,$ !embu,u& d$r$& me,engkung +$ng k&$-. 6!idemio,ogi *-$rkom$ +$ng !$,ing -ering !$d$ !$-ien u-i$ ,$n3u%
deng$n domin$-i -ediki% ,$ki0,$ki *Sering !$d$ dek$de keen$m -$m!$i kede,$!$n *S$ng$% 3$r$ng %er3$di di b$($& u-i$ =8 %$&un.
M+5o/ibro-$rcom$ Si%e o/ In1o,1emen% *gird,e ek-%remi%+ "rend$&< ek-%remi%$- $%$-# *J$r$ng !$d$ b$%$ng %ubu& di ke!$,$ d$n d$er$& ,e&er
Re%ro!eri%oneum d$n rongg$ !eru% . M$ni/e-%$-i k,ini*M$--$ +$ng !er,$&$n mem!erbe-$r *N+eri *kek$mbu&$n -ering beru,$ng * Neo!,$-m$ ke,$- %inggi neo!,$-m$ d$!$% berme%$-%$-i-
ke !$ru d$n %u,$ng
M+5o/ibro-$rcom$ M$kro-ko!i *Neo!,$-m$ %er,e%$k di !ermuk$$n bi$-$n+$ %erdiri d$ri
beber$!$ ber1$ri$-i ken+$, $%$u nodu, ,ebi& ker$- Neo!,$-m$ !$d$ ,$!i-$n ,ebi& d$,$m -ering memben%uk -u$%u m$--$ %ungg$, deng$n m$rgin in/i,%r$%i/. *Neo!,$-m$ ke,$- %inggi -ering di%emuk$n d$er$& nekro-i-
%umor.
M+5o/ibro-$rcom$
Leiom+om$ o/ dee! -o/% %i--ue Leiomiom$ +$ng %er3$di !$d$ 3$ring$n ,un$k d$,$m -om$%ik $%$u re%ro!eri%oneum rongg$ !eru% d$n meru!$k$n 3eni- %umor +$ng -$ng$% ,$ngk$. 6!idemio,ogi *,$ki0,$ki d$n !erem!u$n mem!un+$i !erb$nding$n r$-io +$ng -$m$ *ke,om!ok de($-$ mud$ $%$u !$ru& b$+$ Si%e o/ In1o,1emen% *6k-%remi%$- Re%ro!eri%oneum *Pe,1i*Rongg$ !eru% " me-en%er+ d$n omen%um#
Leiom+om$ o/ dee! -o/% %i--ue M$kro-ko!i *%umor berb$%$- %eg$- *ber($rn$ $bu0$bu !u%i&. *Di$me%er ,eiom+om$ d$ri 3$ring$n ,un$k -om$%ik d$,$m
berki-$r =;0C; cm "r$%$0r$%$ cm# d$n +$ng !$,ing -ering berukur$n ; cm $%$u ,ebi& *ber$% %umor berki-$r =?0;788 g "r$%$0r$%$ C.988 g#
Leiom+o-$rkom$ Tumor g$n$- %erdiri d$ri -e,0-e, +$ng berbed$ -e, o%o% !o,o6!idemio,ogi *%er3$di !$d$ !$ru& b$+$ $%$u ,ebi& %u$ "d$!$% berkemb$ng !$d$ or$ng de($-$ mud$ d$n $n$k0$n$k# Si%e o/ In1o,1emen% *Re%ro!eri%oneum *Pe,1ik *Pembu,u& d$r$& be-$r "umumn+$ 1en$ c$1$ in/erior d$n 1en$ be-$r ek-%remi%$- b$($.
Leiom+o-$rkom$ M$ni/e-%$-i k,ini*N+eri *Sindrom Budd '&i$ri "&e!$%omeg$,i 3$undice d$n $-ci%e-# *di-/ung-i gin3$, *edem$ k$ki
Leim+o-$rcom$ M$kro-ko!i m$--$ berd$ging ($rn$ ber1$ri$-i d$ri $bu0$bu men3$di !u%i& -$m!$i coke,$%. %$m!$k me,ingk$r !$d$ beber$!$ der$3$%. E$ng ,ebi& be-$r -ering %$m!$k !erd$r$&$n nekro-i- $%$u !erub$&$n ki-%ik. %umor berb$%$- %eg$- deng$n b$ik
Leim+o-$rcom$
M+o!eric+%om$ Tumor 3in$k umumn+$ %umor -ubku%$n +$ng %erdiri -e, m+oid berben%uk o1$, -$m!$i -!inde, +$ng muncu, menon3o, ke $r$& Per%umbu&$n !eri1$-ku,$r kon-en%rik . 6!idemio,ogi *-ering !$d$ !er%eng$&$n de($-$
Si%e o/ In1o,1emen% * 3$ring$n -ubku%$n %eru%$m$ di ek-%remi%$- di-%$,
M+o!eric+%om$ M$ni/e-%$-i k,ini*nodu, -o,i%er %$n!$ n+eri -ediki% n+eri *%umbu& ,$mb$% d$n d$!$% %imbu, -e,$m$ ber%$&un0%$&un
M$kro-ko!i *nodu, +$ng cenderung berb$%$- %eg$- deng$n di$m$%er
berukur$n kur$ng d$ri = cm.
M+o!eric+%om$
Angio,eiom+om$ Tumor 3in$k -ubku%$n dermi- d$,$m +$ng %erdiri d$ri o%o% !o,o- m$%ur +$ng menge,i,ingi d$n ber!o%ong$n $n%$r$ -$,ur$n !embu,u& d$r$&. Tumor ini bermor/o,ogi kon%inum deng$n m+o!eric+%om$ d$n m+o/ibrom$. 6!idemio,ogi *Tumor 3$ring$n ,un$k +$ng umum %er3$di "k$-u- %erbe-$r
+$ng di,$!ork$n k$-u- $ngio,eiom+om$ men+umb$ng -eki%$r 7.7 D$ri %o%$, C=.99 k$-u- %umor 3$ring$n ,un$k# *Lebi& -ering !$d$ ($ni%$ *Timbu, !$d$ dek$de ke 7 0 9
Angio,eiom+om$ Si%e o/ In1o,1emen% *ek-%remi%$- %eru%$m$ %ungk$i b$($& d$n d$er$& ,$inn+$
%erm$-uk ke!$,$ d$n b$%$ng %ubu&. M$ni/e-%$-i k,ini*m$--$ keci, !er,$&$n0,$&$n membe-$r bi$-$n+$ d$,$m
beber$!$ %$&un . *N+eri "r$-$ -$ki% di!erburuk o,e& $ngin dingin %ek$n$n
ke&$mi,$n $%$u men-%ru$-i#.
Angio,eiom+om$ M$kro-ko!i *nodu, berb$%$- %eg$- *bu,$% * $bu0$bu !u%i& $%$u cok,$%. *Fu$de nodu, *Di$me%er kur$ng d$ri = cm.
R&$bdom+om$ * %umor me-enc&+m$, 3in$k !$d$ o%o% r$ngk$.
Dik,$-i/ik$-ik$n men3$di = berd$-$rk$n %em!$%: * RM c$rdi$k * RM 6k-%r$c$rdi$k "RM !$d$ de($-$ d$n 3$nin# * RM geni%$,
Adu,% R&$bdom+om$ Tumor 3in$k me-enc&+m$, ,$ngk$ !$d$ di/eren-i$-i o%o% r$ngk$ m$%ur d$n %imbu, !$d$ d$er$& ke!$,$ d$n ,e&er. 6!idemio,ogi U-i$ r$%$0r$%$ $d$,$& 98 %$&un "ki-$r$n -$m!$i ?8 %$&un# deng$n !erb$nding$n : C domin$-i ,$ki0,$ki Si%e o/ in1o,1emen% *muko-$ $erodige-%i1e "/$ring mu,u% rongg$ d$n ,$ring# * 3$ring$n ,un$k ,e&er
Adu,% R&$bdom+om$ M$ni/e-%$-i k,ini*ob-%ruk-i -$,ur$n n$!$- $%$- d$n m$--$ !$d$ muko-$
$%$u 3$ring$n ,un$k M$kro-ko!i *M$--$ *ukur$n cm "ki-$r$n C;0; cm# *berb$%$- %eg$*ber($rn$ cok,$% -$m!$i mer$&0cok,$% *Lembu% *bernodu, $%$u ber,obu-.
Adu,% R&$bdom+om$
)e%$, R&$bdom+om$ Tumor me-enc&+m$, 3in$k +$ng ,$ngk$ +$ng mengg$mb$rk$n di/eren-i$-i o%o% r$ngk$ imm$%ur 6!idemio,ogi *U-i$ r$%$0r$%$ $d$,$& 7 %$&un "ki-$r$n &$ri0;? %$&un#
deng$n =7: C domin$-i ,$ki0,$ki. Si%e- o/ in1o,1emen% *muko-$ d$er$& ke!$,$ d$n ,e&er
)e%$, R&$bdom+om$ M$ni/e-%$-i k,ini*m$--$ %ungg$, +$ng me,ib$%k$n 3$ring$n ,un$k $%$u
muko-$ "dur$-i r$%$0r$%$ ? bu,$n 3$r$k &$ri -$m!$i C> %$&un# M$kro-ko!i *m$--$ %ungg$, *berb$%$- %eg$- *,un$k *ber($rn$ $bu0$bu !u%i& -$m!$i coke,$%0mer$& mud$
deng$n !o%ong$n !ermuk$$n berki,$u.
)e%$, R&$bdom+om$
Geni%$, R&$bdom+om$ Tumor me-enc&+m$, 3in$k ,$ngk$ deng$n %ingk$% di/eren-i$-i o%o% r$ngk$ ,$n3u%$n d$n deng$n !redi,ek-i !$d$ 2$gin$ 6!idemio,ogi *&$m!ir -ec$r$ ek-k,u-i/ di !er%eng$&$n u-i$ !erem!u$n. . *U-i$ r$%$0r$%$ $d$,$& 7= %$&un "ki-$r$n 807? %$&un#.
Si%e o/ in1o,1emen% *1$gin$ *1u,1$ $%$u *,e&er r$&im. *!$r$%e-%icu,$r $%$u e!ididimi- ." !$d$ ,$ki0,$ki 3$r$ng#
Geni%$, R&$bdom+om$ M$ni/e-%$-i k,ini* M$--$ mungkin $-im%om$%ik $%$u %imbu, -$m!$i 70;
%$&un . M$kro-ko!i *M$--$ 1$gin$ !o,+!oid "ukur$n r$%$0r$%$ = cm ki-$r$n C0
cm# *di%u%u!i o,e& muko-$ &$,u-. *berb$%$- %eg$-
S+no1i$, 4em$ngiom$ %umor !embu,u& d$r$& !ro,i/er$-i 3in$k +$ng %imbu, d$,$m !ermuk$$n ,$!i-$n -ino1ium %erm$-uk ru$ng in%r$0$r%iku,$r d$n bur-$ 6!idemio,ogi *S$ng$% 3$r$ng *Keb$n+$k$n !$-ien $n$k $n$k $%$u rem$3$ d$n $d$
kecenderung$n un%uk ,$ki0,$ki. Si%e o/ In1o,1emen% *,u%u% diiku%i ,ebi& 3$r$ng o,e& -iku d$n %$ng$n.
S+no1i$, 4em$ngiom$ M$ni/e-%$-i k,ini*,e-i +$ng %umbu& !er,$&$n *!embengk$k$n d$n e/u-i *N+eri beru,$ng
M$kro-ko!i * %umor berb$%$- %eg$- d$n di/u-. *Konge-%i d$n di,$%$-i !embu,u& d$r$&
2enou- 4em$ngiom$ %erdiri 1en$ ukur$n 1$ri$be, -ering memi,iki dinding o%o% %eb$,. in%r$mu-ku,$r $ngiom$ d$n $ngiom$%o-i- &$m!ir d$!$% %er-u-un -ec$r$ ek-k,u-i/ d$ri 1en$ %$!i bi$-$n+$ berc$m!ur deng$n !embu,u& ,$in. 6!idemio,ogi *24 3$r$ng d$n %imbu, %eru%$m$ !$d$ or$ng de($-$.
Si%e o/ in1o,1emen% *-ubku%$n $%$u 3$ring$n ,un$k +$ng ,ebi& d$,$m d$n
cenderung !$d$ ek-%remi%$-.
2enou- 4em$ngiom$ M$ni/e-%$-i k,ini*%umor +$ng %umbu& !er,$&$n d$n0ber,$ng-ung ,$m$
M$kro-ko!i *%umor berb$%$- %id$k %eg$- d$n *%erdiri d$ri di,$%$-i
ru$ng 1$-ku,$r meng$,$mi konge-%i
Ar%erio1enou- 4em$ngiom$ ,e-i 1$-ku,$r non0neo!,$-%ik di%$nd$i o,e& keber$d$$n d$ri $r%erio1eno-$ -&un%. 6!idemio,ogi *men+er$ng $n$k0$n$k d$n *or$ng de($-$
Si%e o/ In1o,1emen% *Ke!$,$ *Le&er *ek-%remi%$-
Ar%erio1enou- 4em$ngiom$ M$ni/e-%$-i k,iniN+eri &i!er%ro/i ek-%remi%$- g$g$, 3$n%ung Ko$gu,o!$%i "K$-$b$c&0Merri%% -+ndrome#. M$kro-ko!i B$%$- %umor %id$k %eg$- d$n meng$ndung 3um,$& !embu,u& d$r$& keci, d$n be-$r +$ng di,$%$-i
Ar%erio1enou- 4em$ngiom$
L+m!&$ngiom$ Le-i k$1erno-$ ki-%ik 1$-ku,$r 3in$k +$ng %erdiri d$ri di,$%$-i -$,ur$n ,im/$%ik. Beber$!$ k$-u- d$!$% diiden%i/ik$-i d$,$m Sindrom %urner "d$n -indrom m$,/orm$%i/ ,$inn+$# d$n d$!$% di%emuk$n d$,$m $bor%u-. 6!idemio,ogi $n$k d$n -ering %imbu, !$d$ -$$% ,$&ir $%$u -e,$m$ %$&un !er%$m$ ke&idu!$n. Si%e o/ in1o,1emen% *,e&er ke%i$k d$n -e,$ngk$ng$n ",+m!&$ngiom$ ki-%ik# *rongg$ mu,u% b$%$ng %ubu& $%$- %ungk$i d$n !eru% %erm$-uk
me-en%erium d$n re%ro!eri%oneum ",+m!&$ngiom$ k$1erno-um#
L+m!&$ngiom$ M$ni/e-%$-i k,ini!embengk$k$n %$n!$ r$-$ -$ki% M$kro-ko!i *m$--$ mu,%iki-%ik $%$u -!on- rongg$ *meng$ndung c$ir$n +$ng ber$ir -$m!$i -e!er%i -u-u. "($%er+ %o
mi,k+ /,uid#. *,un$k d$n ber/,uk%u$-i !$d$ -$$% di !$,!$-i d$n bi-$
menun3ukk$n !er!ind$&$n org$n -eki%$rn+$ !$d$ d$er$& medi$-%inum $%$u in%r$$bdomin$,
L+m!&$ngiom$
S$rkom$ K$!o-i Tumor endo%e, +$ng bi$-$n+$ %imbu, deng$n ,e-i ku,i% beru!$ berc$k mu,%i!e, !,$k $%$u nodu, %e%$!i 3ug$ d$!$% me,ib$%k$n muko-$ ke,en3$r ge%$& bening d$n org$n 1i-cer$,.
S$rkom$ K$!o-i
S$rkom$ K$!o-i M$kro-ko!i *Le-i !$d$ ku,i% "berc$k !,$k nodu,# ber1$ri$-i d$,$m
ukur$n d$ri +$ng -$ng$% keci, &ingg$ beber$!$ -en%ime%er di$me%ern+$.